Table. 3.

Table. 3.

Patient and transplant characteristics

Characteristics N
Total 17
Male/female 11/6
Age at diagnosis (years)
Median (range) 3.6 (0.2-15.7)
Type of HLH
FHL2 (PRF1) 2
FHL3 (UNC13D) 5
XLP1 1
XLP2 (XIAP) 4
Secondary 5
Age at HCT (years)
Median (range) 5.4 (0.5-17.2)
Donor
Matched sibling donor 1
Unrelated donor 9
Haploidentical family donor 7
Acute GVHD
Grade 2 10
Grade 3 4
Chronic GVHD (evaluable patients) 16
Moderate 1
Severe 3
TRM 2
Disease-free survival at 2 years 90%
Clin Pediatr Hematol Oncol 2021;28:28-38
© 2021 Clin Pediatr Hematol Oncol