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Review Article
Vascular Anomaly: An Updated Review
Clin Pediatr Hematol Oncol 2019;26:6-11.
Published online April 30, 2019
© 2019 Korean Society of Pediatric Hematology-Oncology

Meerim Park

Department of Pediatrics, Center for Pediatric Cancer, National Cancer Center, Goyang, Korea
Correspondence to: Meerim Park
Department of Pediatrics, Center for Pediatric Cancer, National Cancer Center, 323 Ilsan-ro, Ilsandong-gu, Goyang 10408, Korea
Tel: +82-31-920-1240
Fax: +82-31-920-1244
E-mail: meerim@ncc.re.kr
ORCID ID: orcid.org/0000-0002-6847-9447
Received March 24, 2019; Revised April 4, 2019; Accepted April 6, 2019.
This is an Open Access article distributed under the terms of the Creative Commons Attribution Non-Commercial License (http://creativecommons.org/licenses/by-nc/4.0) which permits unrestricted non-commercial use, distribution, and reproduction in any medium, provided the original work is properly cited.
Abstract
Vascular anomalies comprise a heterogeneous group of disorders characterized by abnormal growth or development of blood vessels. Diagnosis of vascular anomalies is often challenging due to the large variety of conditions, which exhibit phenotypic heterogeneity and a wide range of symptomology and severity. Accurate diagnosis is crucial for appropriate evaluation and management, often requiring multidisciplinary specialists. Recent interdisciplinary collaboration has led to collaborative studies and their outcomes are being prospectively evaluated. While there is still a role for surgical intervention in various vascular anomalies, discoveries of pharmacologic agents effective in treating vascular anomalies have broadened our medical therapeutic options. This paper focuses on vascular anomaly issues often seen by the pediatricians and reviews the clinical pearls on infantile hemangiomas, lymphatic malformations, venous malformations, and arteriovenous malformations.
Keywords: Vascular anomalies, Heterogeneity, Diagnosis, Therapeutic option
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  • Meerim Park